%0 Journal Article %T Extranodal NK/T cell lymphoma-associated hemophagocytic syndrome: where do we stand? %A Huang, Rui %A He, Ying-Zhi %A Lai, Qiu-Yu %A Wang, Liang %J Annals of Lymphoma %D 2018 %B 2018 %9 %! Extranodal NK/T cell lymphoma-associated hemophagocytic syndrome: where do we stand? %K %X Hemophagocytic lymphohistiocytosis (HLH), first reported as “ familial hemophagocytic reticulosis ” by Farquhar JW in 1952, is a rare life-threatening disorder characterized by overwhelming immune and inflammation activation, and “cytokine storm” (1-5). HLH can be roughly categorized as primary HLH (pHLH), which is inherited, or secondary HLH (sHLH) occurring in a context of infection, autoimmune diseases or malignancies. %U https://aol.amegroups.org/article/view/4525 %V 2 %P %@ 2616-2695